Anaesthesia in patients with mucopolysaccharidoses (MPS)
Keywords
Regional anaesthesia, Mucopolysaccharidosis, MPS VI (Maroteaux-Lamy), MPS IV (Morquio), MPS III (San Filippo), MPS II (Hunter), MPS I (Hurler), Local anaesthesia, General anaesthesia, Anaesthetic assessment
Surgery in disorders of fatty acid oxidation (excluding MCADD)
This protocol covers children with all the fat oxidation disorders excluding MCAD deficiency.
Surgery in MCADD
Surgery in organic acidaemias
This protocol covers organic acidaemias and Maple Syrup Urine Disease (MSUD)
Surgery in those at risk of hypoglycaemia
This covers those with glycogen storage disease, disorders of gluconeogenesis and ketotic hypoglycaemia.