TEMPLE (Tools Enabling Metabolic Parents LEarning) are a set of teaching slides and booklets that provide essential information about different inherited metabolic disorders that require special diets as part of their management. These teaching tools are aimed at parents who may have an infant or child that has been recently diagnosed with a disorder, but they are also useful when teaching children, extended family members, child minders, nursery workers and school team.
They are not designed to replace dietary information that may be given by a dietitian in clinic.
They have been developed by a team of experienced clinical and research metabolic dietitians from the UK who are members of the British Inherited Metabolic Disease Group (BIMDG).
The team are Rachel Skeath, Karen van Wyk, Pat Portnoi and Anita MacDonald. The group is facilitated by Heidi Chan from Nutricia.
Each module produced is reviewed by a consultant clinician who is a member of the BIMDG.
(N.B. These teaching tools are a modified version of the original TEMPLE information package designed by Dr's Wendel and Burgard from Heidelberg, Germany)
Please note:
to view TEMPLE presentations as intended (with animation), please download and SAVE the PDF file to users own computer. Then open the downloaded file from your computer.
TEMPLE Guides
- Arginase deficiency
- Argininosuccinic aciduria
- CACT (Carnitine Acylcarnitine Translocase Deficiency)
- Carnitine Palmitoyl Transferase 1 Deficiency
- Carnitine Palmitoyl Transferase II Deficiency
- Citrullinaemia
- GA1 (glutaric aciduria type 1)
- Galactosaemia
- GSD Ia (Glycogen Storage Disease Ia)
- GSD Ib (Glycogen Storage Disease Ib)
- GSD III (Glycogen Storage Disease III)
- HCU (Homocystinuria)
- IVA (Isovaleric Acidaemia)
- LCHAD Deficiency
- MCADD (medium chain acyl-CoA dehydrogenase deficiency)
- MMA (Methyl Malonic Acidaemia)
- MSUD (Maple Syrup Urine Disease)
- OTC (Ornithine transcarbamylase deficiency)
- PKU (Phenylketonuria)
- Propionic Acidaemia (PA)
- Tyrosinaemia Type 1
- Tyrosinaemia Type 2
- VLCADD (very long chain acyl-CoA dehydrogenase deficiency)
Arginase deficiency
Information for families following a new diagnosis (Version 3, 2025)
Argininosuccinic aciduria
Information for families following a new diagnosis (Version 3, 2025)
CACT (Carnitine Acylcarnitine Translocase Deficiency)
Information for families (Version 4 - 2025)
Carnitine Palmitoyl Transferase 1 Deficiency
Information for families following a new diagnosis
Carnitine Palmitoyl Transferase II Deficiency
Information for families following a new diagnosis (Version 4, 2025)
Citrullinaemia
Information for families following a new diagnosis (Version 3, 2025)
GA1 (glutaric aciduria type 1)
Information for families following a new diagnosis (Version 4, 2025)
Galactosaemia
Information for families following a new diagnosis (Version 3, 2025)
GSD Ia (Glycogen Storage Disease Ia)
Information for families following a new diagnosis (2025)
GSD Ib (Glycogen Storage Disease Ib)
Information for families following a new diagnosis (2025)
GSD III (Glycogen Storage Disease III)
Information for families following a new diagnosis (2025)
HCU (Homocystinuria)
Information for families following a new diagnosis (Version 5, 2025)
IVA (Isovaleric Acidaemia)
Information for families following a new diagnosis (2025)
LCHAD Deficiency
Information for families following a new diagnosis (Version 4, 2025)
MCADD (medium chain acyl-CoA dehydrogenase deficiency)
Information for families following a new diagnosis (Version 4, 2025)
MMA (Methyl Malonic Acidaemia)
Information for families following a new diagnosis (Version 5, 2025)
MSUD (Maple Syrup Urine Disease)
Information for families following a new diagnosis (Version 4, 2025)
OTC (Ornithine transcarbamylase deficiency)
Information for families following a new diagnosis (Version 3, 2025)
PKU (Phenylketonuria)
Information for families following a new diagnosis (Version 4, 2025)
Propionic Acidaemia (PA)
Information for families following a new diagnosis (Version 4, 2025)
Tyrosinaemia Type 1
Information for families following a new diagnosis (Version 4, 2025)
Tyrosinaemia Type 2
Information for families following a new diagnosis (Version 4, 2025)
VLCADD (very long chain acyl-CoA dehydrogenase deficiency)
Information for families following a new diagnosis (Version 3, 2025)